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Title Systemic fibroinflammatory disorders / Augusto Vaglio, editor
Published Cham, Switzerland : Springer, 2017


Description 1 online resource
Series Rare diseases of the immune system
Rare diseases of the immune system.
Contents Preface -- 1 Genetics of fibro-inflammatory disorders -- 2 Basic mechanisms linking inflammation and fibrosis -- 3 Histopathology of systemic fibro-inflammatory disorders -- 4 IgG4-related disorders: clinical and therapeutic aspects -- 5 IgG4-related disorders: pathophysiology -- 6 IgG4-related nephropathy -- 7 Autoimmune (IgG4-related) pancreatitis and sclerosing cholangitis -- 8 Sclerosing forms of autoimmune thyroiditis: from Hashimoto?s to Riedel?s to IgG4-related forms -- 9 Chronic periaortitis/retroperitoneal fibrosis: overview -- 10 Diffuse periaortitis -- 11 Treatment of chronic periaortitis/retroperitoneal fibrosis -- 12 Mediastinal fibrosis -- 13 Erdheim-Chester disease -- 14 Nephrogenic systemic fibrosis -- 15 Sclerosing mesenteritis -- 16 Malignant diseases mimicking retroperitoneal fibrosing disorders -- Subject Index
Summary This book provides detailed information on the nosology, pathology, pathogenesis, clinical presentation, diagnosis and treatment of fibro-inflammatory disorders, rare diseases that often display systemic organ involvement. Among the conditions considered are IgG4-related disease, sclerosing cholangitis, Hashimoto?s and Riedel?s thyroiditis, retroperitoneal fibrosis/chronic periaortitis, mediastinal fibrosis, Erdheim-Chester disease, gadolinium-induced fibrosis, and sclerosing mesenteritis. This group of entities is still poorly defined and is characterized by the common denominator of chronic inflammatory infiltrate admixed with abundant fibrosis. IgG4-related disease is the prototypical example. Systemic Fibroinflammatory Disorders is the first book to draw together information on these conditions. As these diseases often require an interdisciplinary approach, the book is addressed to specialists of different disciplines, especially internists, rheumatologists, nephrologists, clinical immunologists, and hematologists
Notes Includes index
Bibliography Includes bibliographical references and index
Notes Online resource; title from PDF title page (SpringerLink, viewed January 17, 2017)
In Springer eBooks
Subject Fibrosis.
Fibrosis -- physiopathology
Inflammation -- physiopathology
Autoimmune Diseases -- physiopathology
Renal medicine & nephrology.
HEALTH & FITNESS -- Diseases -- General.
MEDICAL -- Clinical Medicine.
MEDICAL -- Diseases.
MEDICAL -- Evidence-Based Medicine.
MEDICAL -- Internal Medicine.
Form Electronic book
Author Vaglio, Augusto, editor
ISBN 9783319413495